Clinical and laboratory findings

Anti-ARS

Anti-CADM-140/MDA5

Anti-Mi-2

Anti-p155/TIF1-γ

Typical DM rash

V-sign or Shawl-sign

Muscle weakness

×

Elevation of CK

×

Fever

×

×

Arthritis

×

×

Rapidly progressive ILD

×

×

×

Chronic ILD

×

×

×

Malignancy

×

ANA (FANA) positive (%)

×

×